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Ep. 30 | Weight Health in Cystic Fibrosis: A Comprehensive Approach using Body Composition

in-the-know-with-nina

podcast

Episode Summary

In this episode of In the Know with Nina, Dr. Nina Crowley is joined by Sarah Hendrix, a certified advanced cystic fibrosis dietitian at the Medical University of South Carolina. Together, they explore how advancements in cystic fibrosis (CF) treatment—specifically highly effective modulator therapies—have shifted the focus from underweight and malnutrition to new challenges like overweight and obesity in CF patients.

Sarah shares how body composition is becoming a vital tool in managing weight-related concerns in CF. The discussion covers the significance of differentiating fat mass from fat-free mass, how weight-bearing exercise can improve clinical outcomes, and the importance of adjusting medications and nutrition plans accordingly. With this new weight paradigm, Sarah emphasizes the need for comprehensive care that includes psychological support, personalized nutrition, and consistent monitoring.

Key Takeaways

Modulator therapy has led to unintended weight gain in many individuals with CF.
Body composition analysis is essential for distinguishing between fat mass and fat-free mass, especially as BMI alone is no longer adequate.
CF patients often have low physical activity levels, making strength training a new priority.
Medication dose adjustments do not always result in weight loss and may impact lung function.
Understanding resting energy expenditure and fat-free mass helps tailor better care strategies.
Psychological effects and weight stigma are emerging concerns as patients navigate new body changes.

About Sarah Hendrix, MS, RD

Sarah Hendrix is a certified advanced cystic fibrosis dietitian at the Medical University of South Carolina, where she has worked for over a decade. She provides care to both pediatric and adult CF patients and is a key member of the interdisciplinary care team. Sarah is passionate about using body composition data to inform patient care and is involved in national conversations about advancing CF nutrition practices through conferences and consortium work.